Retroperitoneal fibrosis – a report of five cases
نویسندگان
چکیده
منابع مشابه
Retroperitoneal fibrosis – a report of five cases
Retroperitoneal fibrosis (RPF) is a rare disease, characterized by inflammation and deposition of fibrotic tissue in the vicinity of the abdominal aorta and iliac arteries. We present a report of five patients admitted to our department between January 2014 and February 2017, diagnosed with RPF. Abdominal pain was the most common presenting symptom; however, in one patient, RPF was identified a...
متن کاملRetroperitoneal fibrosis: a case report
Retroperitoneal fibrosis is characterized by development of extensive fibrosis, leading to entrapment and obstruction of retroperitoneal structures, notably the ureters. In most cases, the etiology is unknown. It is occasionally associated with autoimmune diseases. Response to corticosteroids and immunosuppressive therapy suggest it is probably immunologically mediated. The symptoms and signs a...
متن کاملidiopathic retroperitoneal fibrosis: a case report and review of articles
idiopathic retroperitoneal fibrosis is a rare disorder of an unknown etiology characterized by an inflammatory proliferative fibrosing process that may involve the ureters in 80-100% of cases. â the present study was carried on a 38 years old man who was admitted to imam khomeini hospital with severe abdominal pain and renal failure. abdominal mri showed encasement of abdominal aorta and bilate...
متن کاملSurgical treatment of idiopathic mediastinal fibrosis: report of five cases.
Idiopathic mediastinal fibrosis is a rare disease of unknown aetiology. It is a benign condition in which abnormal proliferation of fibrous tissue occurs within the mediastinum, leading to constriction and obliteration of local structures, particularly the great veins. It is a rare cause of superior vena caval obstruction (1-2%) but one that is potentially amenable to surgical palliation. The r...
متن کاملREPORT OF FOUR CASES OF FAMILIAL IDIOPATHIC PULMONARY FIBROSIS
A 25 year old male and his 46 year old aunt presented with shortness of breath and a dramatic response to steroids. The other two patients are sisters with more advanced disease. One of these responded partially to steroids, while the other died within 4 months of treatment. The genetic basis and pathogenesis are discussed.
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
ژورنال
عنوان ژورنال: Reumatologia/Rheumatology
سال: 2017
ISSN: 0034-6233
DOI: 10.5114/reum.2017.68914